IMED3001 Lecture Notes - Lecture 23: Hypereosinophilic Syndrome, Hypertrophic Cardiomyopathy, Myotonic Dystrophy
26 Mar 2020
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Idiopathic (dcm, hcm, rcm: familial (dcm, hcm, eosinophilic endomyocardial disease (rcm, endomyocardial fibrosis (rcm, arrhythmogenic cardiomyopathy. Infective (dcm: metabolic (dcm, familial storage disease (dcm, rcm, deficiency (dcm, connective tissue disorders (dcm, sle, pan, ra, pss, dm. Infiltrations and granulomas (rcm, dcm: amyloidosis, sarcoidosis, malignancy, neuromuscular (dcm, muscular dystrophy, myotonic dystrophy, Friedreich"s ataxia: sensitivity and toxic reaction (dcm, alcohol, radiation, drugs-adriamycin, cyclophosphamide, 5fu, peripartum heart disease (dcm) Endomyocardial biopsy: for diagnosis and management of patients with myocardial disease and in cardiac transplant recipients, bioptome. It is inserted transvenously into the right side of the heart and a small piece of septal myocardium is obtained and analysed. Morphological patterns: 90% of cardiomyopathies, hypertrophy and dilatation of all four chambers. Restrictive cardiomyopathy: abnormal diastolic function, excessively rigid left ventricular wall, which impedes ventricular filling during diastole, diseases that affect the myocardium, amyloid disease of the heart, radiation fibrosis fibrosis, sarcoidosis, metastatic tumours or deposition of metabolites.
