DENT3060 Lecture Notes - Lecture 14: Cleidocranial Dysostosis, Amelogenesis Imperfecta, Ectodermal Dysplasia
Document Summary
Syndromes: prevent, interceptive tx, restore, pros, ortho, implant, multidisciplinary management: ectodermal dysplasia (ed): inherited disorder of ectoderm; many types/modes inheritance, co(cid:374)ical (cid:858)va(cid:373)pire(cid:859) teeth, (cid:373)issi(cid:374)g teeth, cleft lip/palate, down syndrome (ds) Microdontia: esp. peg lateral (all teeth = ai hypoplastic type?) Molar-incisor hypomineralisation (mih): ce(cid:374)tral i(cid:374)cisors, 6(cid:859)s (few months-2/3yo: ameloblasts temperature-sensitive, enamel forms from cusp tips down crown, clinical issues: living standards, neonatal care, education, ses), f. Amelogenesis imperfecta (ai): disorder of enamel not associated with systemic disease: usu. all teeth affected, multiple modes inheritance, hypoplastic, hypomaturation, hypocalcification.