NURS 287 Lecture Notes - Lecture 10: Von Willebrand Disease, Acute Myeloid Leukemia, Chronic Myelogenous Leukemia
28 Apr 2013
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Document Summary
Hemophilia is a sex-linked recessive genetic disorder caused by defective or deficient coagulation factor. The two major forms of hemophilia, which can occur in mild to severe forms, are hemophilia a and hemophilia b. Von willebrand disease is a related disorder involving a deficiency of the von willebrand coagulation protein. Replacement of deficient clotting factors is the primary means of supporting a patient with hemophilia. In addition to treating acute crises, replacement therapy may be given before surgery and before dental care as a prophylactic measure. Home management is a primary consideration for the patient with hemophilia because the disease follows a progressive, chronic course. The patient with hemophilia must be taught to recognize disease-related problems and to learn which problems can be resolved at home and which require hospitalization. Disseminated intravascular coagulation (dic) is a serious bleeding and thrombotic disorder. It results from abnormally initiated and accelerated clotting.
